翻訳と辞書 Words near each other ・ Uroplatus phantasticus ・ Uroplatus sameiti ・ Uroplatus sikorae ・ Uroplectes ・ Uroplectes formosus ・ Uroplectes lineatus ・ Uroplectes olivaceus ・ Uropod ・ Uropod (immunology) ・ Uropodidae ・ Uropolystigma ・ Uroporphyrinogen ・ Uroporphyrinogen I ・ Uroporphyrinogen III ・ Uroporphyrinogen III decarboxylase ・ Uroporphyrinogen III synthase ・ Uroporphyrinogen-III C-methyltransferase ・ Uropsalis ・ Uropsilinae ・ Uropteryginae ・ Uropterygius ・ Uropterygius concolor ・ Uropterygius fasciolatus ・ Uropterygius fuscoguttatus ・ Uropterygius genie ・ Uropterygius golanii ・ Uropterygius inornatus ・ Uropterygius kamar ・ Uropterygius macrocephalus ・ Uropterygius macularius Dictionary Lists mini英和辞書 mini和英辞書 Webster 1913 Latin-English FOLDOC Wikipedia English ウィキペディア

翻訳と辞書　辞書検索 [ 開発暫定版 ] スポンサード リンク Uroporphyrinogen III synthase ： ウィキペディア英語版 Uroporphyrinogen III synthase Uroporphyrinogen III synthase is an enzyme involved in the metabolism of the cyclic tetrapyrrole compound porphyrin. It is involved in the conversion of hydroxymethyl bilane into uroporphyrinogen III. This enzyme catalyses the inversion of the final pyrrole unit (ring D) of the linear tetrapyrrole molecule, linking it to the first pyrrole unit (ring A), thereby generating a large macrocyclic structure, uroporphyrinogen III. The enzyme folds into two alpha/beta domains connected by a beta-ladder, the active site being located between the two domains. ==Pathology== A deficiency is associated with Gunther's disease, also known as congenital erythropoietic porphyria (CEP). This is an autosomal recessive inborn error of metabolism that results from the markedly deficient activity of uroporphyrinogen III synthase . 抄文引用元・出典: フリー百科事典『 ウィキペディア（Wikipedia）』 ■ウィキペディアで「Uroporphyrinogen III synthase」の詳細全文を読む スポンサード リンク 翻訳と辞書 : 翻訳のためのインターネットリソース Copyright(C) kotoba.ne.jp 1997-2016. All Rights Reserved.